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Material Type: Artigo
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Long-term outcomes of 176 patients with X-linked hyper-IgM syndrome treated with or without hematopoietic cell transplantationMaria Teresa de la Morena David Leonard; Troy R Torgerson; Otavio Cabral Marques; Mary Anne Slatter; Asghar Aghamohammadi; Sharat Chandra; Luis Murguia Favela; Francisco A Bonilla; Maria Kanariou; Rongras Damrongwatanasuk; Caroline Y Kuo; Christopher C Dvorak; Isabelle Meyts; Karin Chen; Lisa Kobrynski; Neena Kapoor; Darko Richter; Daniela DiGiovanni; Fatima Dhalla; Evangelia Farmaki; Carsten Speckmann; Teresa Español; Anna YU Shcherbina; Imelda Celine Guerra Hanson; Jiri Litzman; John M Routes; Melanie Wong; Ramsay Fuleihan; Suranjith L Seneviratne; Trudy N Small; Ales Janda; Liliana Bezrodnik; Reinhard Seger; Andrea Gomez Raccio; John David M Edgar; Janet Chou; Jordan Keith Abbott; Joris van Montfrans; Luis Ignacio González Granado; Nancy Bunin; Necil Kutukculer; Paul Gray; Gisela Seminario; Srdjan Pasic; Victor Aquino; Christian Wysocki; Hassan Abolhassani; Morna Dorsey; Charlotte Cunningham Rundles; Alan Paul Knutsen; John William Sleasman; Beatriz Tavares Costa Carvalho; Antonio Condino-Neto; Eyal Grunebaum; Helen Chapel; Hans Dieter Ochs; Alexandra Hult Filipovich; Mort Cowan; Andrew Gennery; Andrew James Cant; Luigi D Notarangelo; Chaim M RoifmanJournal of Allergy and Clinical Immunology v. 139, n. 4, p. 1282-1292, 2017Philadelphia 2017Localização: ICB - Inst. Ciências Biomédicas (PC ICB BMI SEP 2017 )(Acessar) |
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Material Type: Artigo
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Dominant-negative mutations in the DNA-binding domain of STAT3 cause hyper-IgE syndromeMinegishi, Yoshiyuki ; Saito, Masako ; Tsuchiya, Shigeru ; Tsuge, Ikuya ; Takada, Hidetoshi ; Hara, Toshiro ; Kawamura, Nobuaki ; Ariga, Tadashi ; Pasic, Srdjan ; Stojkovic, Oliver ; Metin, Ayse ; Karasuyama, HajimeNature (London), 2007-08, Vol.448 (7157), p.1058-1062 [Periódico revisado por pares]London: Nature PublishingTexto completo disponível |
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Material Type: Artigo
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Association of Antiphospholipid Antibodies with Clinical Manifestations in Children with Systemic Lupus ErythematosusPetrovic, Gordana ; Pasic, Srdjan ; Soldatovic, IvanJournal of clinical medicine, 2023-02, Vol.12 (4), p.1424 [Periódico revisado por pares]Switzerland: MDPI AGTexto completo disponível |
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Material Type: Artigo
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Mechanisms of redox balance and inflammatory response after the use of methylprednisolone in children with multisystem inflammatory syndrome associated with COVID-19Krasic, Stasa ; Vukomanovic, Vladislav ; Ninic, Sanja ; Pasic, Srdjan ; Samardzija, Gordana ; Mitrovic, Nemanja ; Cehic, Maja ; Nesic, Dejan ; Bajcetic, MilicaFrontiers in immunology, 2023-08, Vol.14, p.1249582-1249582 [Periódico revisado por pares]Frontiers Media S.ATexto completo disponível |
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Material Type: Artigo
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Human Tyrosine Kinase 2 Deficiency Reveals Its Requisite Roles in Multiple Cytokine Signals Involved in Innate and Acquired ImmunityMinegishi, Yoshiyuki ; Saito, Masako ; Morio, Tomohiro ; Watanabe, Ken ; Agematsu, Kazunaga ; Tsuchiya, Shigeru ; Takada, Hidetoshi ; Hara, Toshiro ; Kawamura, Nobuaki ; Ariga, Tadashi ; Kaneko, Hideo ; Kondo, Naomi ; Tsuge, Ikuya ; Yachie, Akihiro ; Sakiyama, Yukio ; Iwata, Tsutomu ; Bessho, Fumio ; Ohishi, Tsutomu ; Joh, Kosuke ; Imai, Kohsuke ; Kogawa, Kazuhiro ; Shinohara, Miwa ; Fujieda, Mikiya ; Wakiguchi, Hiroshi ; Pasic, Srdjan ; Abinun, Mario ; Ochs, Hans D. ; Renner, Eleonore D. ; Jansson, Annette ; Belohradsky, Bernd H. ; Metin, Ayse ; Shimizu, Norio ; Mizutani, Shuki ; Miyawaki, Toshio ; Nonoyama, Shigeaki ; Karasuyama, HajimeImmunity (Cambridge, Mass.), 2006-11, Vol.25 (5), p.745-755 [Periódico revisado por pares]United States: Elsevier IncTexto completo disponível |
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Material Type: Artigo
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Case Report: Early Onset Systemic Lupus Erythematosus Due to Hereditary C1q Deficiency Treated With Fresh Frozen PlasmaZecevic, Milica ; Minic, Aleksandra ; Pasic, Srdjan ; Perovic, Vladimir ; Prohászka, ZoltánFrontiers in pediatrics, 2021-12, Vol.9, p.756387 [Periódico revisado por pares]Switzerland: Frontiers Media S.ATexto completo disponível |
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Material Type: Artigo
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Analysis of cardiac manifestation and treatment of multisystem inflammatory syndrome in children related to SARS-CoV-2Krasic, Stasa ; Ninic, Sanja ; Prijic, Sergej ; Popovic, Sasa ; Pasic, Srdjan ; Petrovic, Gordana ; Zec, Boris ; Ristic, Snezana ; Nesic, Dejan ; Nikolic, Luka ; Vukomanovic, VladislavBiomolecules & biomedicine, 2023-03, Vol.23 (2), p.335-343 [Periódico revisado por pares]Bosnia and Herzegovina: Association of Basic Medical Sciences of Federation of Bosnia and HerzegovinaTexto completo disponível |
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Material Type: Artigo
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Central Nervous System Involvement in Hemophagocytic Lymphohistiocytosis: A Single-Center ExperienceJovanovic, Ankica, MD ; Kuzmanovic, Milos, MD ; Kravljanac, Ruzica, MD ; Micic, Dragan, MD ; Jovic, Milena, MD ; Gazikalovic, Slobodan, MD ; Pasic, Srdjan, MDPediatric neurology, 2014-03, Vol.50 (3), p.233-237 [Periódico revisado por pares]United States: Elsevier IncTexto completo disponível |
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Material Type: Artigo
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Common variable immunodeficiency classification by quantifying T-cell receptor and immunoglobulin κ-deleting recombination excision circlesKamae, Chikako, MD ; Nakagawa, Noriko, MD, PhD ; Sato, Hiroki, MS ; Honma, Kenichi, MD ; Mitsuiki, Noriko, MD ; Ohara, Osamu, PhD ; Kanegane, Hirokazu, MD, PhD ; Pasic, Srdjan, MD, PhD ; Pan-Hammarström, Qiang, MD, PhD ; van Zelm, Menno C., PhD ; Morio, Tomohiro, MD, PhD ; Imai, Kohsuke, MD, PhD ; Nonoyama, Shigeaki, MD, PhDJournal of allergy and clinical immunology, 2013-05, Vol.131 (5), p.1437-1440.e5 [Periódico revisado por pares]United States: Mosby, IncTexto completo disponível |
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Material Type: Artigo
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Expansion of immunoglobulin-secreting cells and defects in B cell tolerance in Rag-dependent immunodeficiencyWalter, Jolan E ; Rucci, Francesca ; Patrizi, Laura ; Recher, Mike ; Regenass, Stephan ; Paganini, Tiziana ; Keszei, Marton ; Pessach, Itai ; Lang, Philipp A ; Poliani, Pietro Luigi ; Giliani, Silvia ; Al-Herz, Waleed ; Cowan, Morton J ; Puck, Jennifer M ; Bleesing, Jack ; Niehues, Tim ; Schuetz, Catharina ; Malech, Harry ; DeRavin, Suk See ; Facchetti, Fabio ; Gennery, Andrew R ; Andersson, Emma ; Kamani, Naynesh R ; Sekiguchi, JoAnn ; Alenezi, Hamid M ; Chinen, Javier ; Dbaibo, Ghassan ; ElGhazali, Gehad ; Fontana, Adriano ; Pasic, Srdjan ; Detre, Cynthia ; Terhorst, Cox ; Alt, Frederick W ; Notarangelo, Luigi DThe Journal of experimental medicine, 2010-07, Vol.207 (7), p.1541-1554 [Periódico revisado por pares]United States: The Rockefeller University PressTexto completo disponível |