Result Number | Material Type | Add to My Shelf Action | Record Details and Options |
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Material Type: Artigo
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Human CD40 ligand deficiency dysregulates the macrophage transcriptome causing functional defects that are improved by exogenous IFN-γCabral-Marques, Otavio, PhD ; Ramos, Rodrigo Nalio, PhD ; Schimke, Lena F., MD ; Khan, Taj Ali, PhD ; Amaral, Eduardo Pinheiro, PhD ; Barbosa Bomfim, Caio César, MSc ; Junior, Osvaldo Reis, MSc ; França, Tabata Takahashi, MSc ; Arslanian, Christina, BSc ; Carola Correia Lima, Joanna Darck, MSc ; Weber, Cristina Worm, MD ; Ferreira, Janaíra Fernandes, MD ; Tavares, Fabiola Scancetti, MD ; Sun, Jing, MD ; D'Imperio Lima, Maria Regina, PhD ; Seelaender, Marília, PhD ; Garcia Calich, Vera Lucia, PhD ; Marzagão Barbuto, José Alexandre, MD, PhD ; Costa-Carvalho, Beatriz Tavares, MD, PhD ; Riemekasten, Gabriela, MD ; Seminario, Gisela, MD ; Bezrodnik, Liliana, MD ; Notarangelo, Luigi, MD ; Torgerson, Troy R., MD, PhD ; Ochs, Hans D., MD ; Condino-Neto, Antonio, MD, PhDJournal of allergy and clinical immunology, 2017-03, Vol.139 (3), p.900-912.e7 [Periódico revisado por pares]United States: Elsevier IncTexto completo disponível |
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Material Type: Artigo
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Human CD40 ligand deficiency dysregulates the macrophage transcriptome causing functional defects that are improved by exogenous IFN-γOtavio Cabral-Marques Rodrigo Nalio Ramos; Lena Friederick Schimke; Taj Ali Khan; Eduardo Pinheiro Amaral; Caio César Barbosa Bomfim; Osvaldo Reis Junior; Tabata Takahashi França; Christina Arslanian Kubo; Joanna Darck Carola Correia Lima; Cristina Worm Weber; Janaíra Fernandes Ferreira; Fabiola Scancetti Tavares; Jing Sun; Maria Regina D'Império Lima; Marília Seelaender; Vera Lucia Garcia Calich; José Alexandre Marzagão Barbuto; Beatriz Tavares Costa-Carvalho; Gabriela Riemekasten; Gisela Seminario; Liliana Bezrodnik; Luigi Notarangelo; Troy R Torgerson; Hans D Ochs; Antonio Condino-NetoJournal of Allergy and Clinical Immunology Philadelphia v. 139, n. 3, p. 900-912, 2017Philadelphia 2017Localização: ICB - Inst. Ciências Biomédicas (PC ICB BMI SEP 2017 )(Acessar) |
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Material Type: Artigo
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Human OTULIN haploinsufficiency impairs cell-intrinsic immunity to staphylococcal α-toxinSpaan, András N ; Neehus, Anna-Lena ; Laplantine, Emmanuel ; Staels, Frederik ; Ogishi, Masato ; Seeleuthner, Yoann ; Rapaport, Franck ; Lacey, Keenan A ; Van Nieuwenhove, Erika ; Chrabieh, Maya ; Hum, David ; Migaud, Mélanie ; Izmiryan, Araksya ; Lorenzo, Lazaro ; Kochetkov, Tatiana ; Heesterbeek, Dani A C ; Bardoel, Bart W ; DuMont, Ashley L ; Dobbs, Kerry ; Chardonnet, Solenne ; Heissel, Søren ; Baslan, Timour ; Zhang, Peng ; Yang, Rui ; Bogunovic, Dusan ; Wunderink, Herman F ; Haas, Pieter-Jan A ; Molina, Henrik ; Van Buggenhout, Griet ; Lyonnet, Stanislas ; Notarangelo, Luigi D ; Seppänen, Mikko R J ; Weil, Robert ; Seminario, Gisela ; Gomez-Tello, Héctor ; Wouters, Carine ; Mesdaghi, Mehrnaz ; Shahrooei, Mohammad ; Bossuyt, Xavier ; Sag, Erdal ; Topaloglu, Rezan ; Ozen, Seza ; Leavis, Helen L ; van Eijk, Maarten M J ; Bezrodnik, Liliana ; Blancas Galicia, Lizbeth ; Hovnanian, Alain ; Nassif, Aude ; Bader-Meunier, Brigitte ; Neven, Bénédicte ; Meyts, Isabelle ; Schrijvers, Rik ; Puel, Anne ; Bustamante, Jacinta ; Aksentijevich, Ivona ; Kastner, Daniel L ; Torres, Victor J ; Humblet-Baron, Stéphanie ; Liston, Adrian ; Abel, Laurent ; Boisson, Bertrand ; Casanova, Jean-LaurentScience (American Association for the Advancement of Science), 2022-06, Vol.376 (6599), p.eabm6380-eabm6380 [Periódico revisado por pares]United States: The American Association for the Advancement of ScienceTexto completo disponível |
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Material Type: Artigo
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First report of the hyper-IgM syndrome registry of the Latin American Society for Immunodeficiencies novel mutations, unique infections, and outcomesOtavio Cabral-Marques Stefanie Klaver; Lena Schimke; Évelyn H Ascendino; Taj Ali Khan; Paulo Vitor Soeiro Pereira; Angela Falcai; Alexander Vargas-Hernández; Leopoldo Santos-Argumedo; Liliana Bezrodnik; Ileana Moreira; Gisela Seminario; Daniela Di Giovanni; Andrea Gómez Raccio; Oscar Porras; Cristina Worm Weber; Janaíra Fernandes Ferreira; Fabiola Scancetti Tavares; Elisa de Carvalho; Claudia França Cavalcante Valente; Gisele Kuntze; Miguel Galicchio; Alejandra King; Nelson Augusto Rosário-Filho; Milena Baptistella Grota; Maria Marluce dos Santos Vilela; Regina Sumiko Watanabe Di Gesu; Simone Lima; Leiva de Souza Moura; Eduardo Talesnik; Eli Mansour; Persio Roxo Junior; Juan Carlos Aldave; Ekaterine Goudouris; Fernanda Pinto-Mariz; Laura Berrón-Ruiz; Tamara Staines-Boone; Wilmer O. Córdova Calderón; María del Carmen Zarate-Hernández; Anete S Grumach; Ricardo Sorensen; Anne Durandy; Troy R Torgerson; Beatriz Tavares Costa Carvalho; Francisco Espinosa-Rosales; Hans D Ochs; Antonio Condino-NetoJournal of Clinical Immunology New York v. 34, n. 2, p. 146-156, 2014New York 2014Localização: FMRP - Fac. Medicina de Ribeirão Preto (pcd 2496917 Estantes Deslizantes ) e outros locais(Acessar) |
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Material Type: Artigo
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Long-term outcomes of 176 patients with X-linked hyper-IgM syndrome treated with or without hematopoietic cell transplantationMaria Teresa de la Morena David Leonard; Troy R Torgerson; Otavio Cabral Marques; Mary Anne Slatter; Asghar Aghamohammadi; Sharat Chandra; Luis Murguia Favela; Francisco A Bonilla; Maria Kanariou; Rongras Damrongwatanasuk; Caroline Y Kuo; Christopher C Dvorak; Isabelle Meyts; Karin Chen; Lisa Kobrynski; Neena Kapoor; Darko Richter; Daniela DiGiovanni; Fatima Dhalla; Evangelia Farmaki; Carsten Speckmann; Teresa Español; Anna YU Shcherbina; Imelda Celine Guerra Hanson; Jiri Litzman; John M Routes; Melanie Wong; Ramsay Fuleihan; Suranjith L Seneviratne; Trudy N Small; Ales Janda; Liliana Bezrodnik; Reinhard Seger; Andrea Gomez Raccio; John David M Edgar; Janet Chou; Jordan Keith Abbott; Joris van Montfrans; Luis Ignacio González Granado; Nancy Bunin; Necil Kutukculer; Paul Gray; Gisela Seminario; Srdjan Pasic; Victor Aquino; Christian Wysocki; Hassan Abolhassani; Morna Dorsey; Charlotte Cunningham Rundles; Alan Paul Knutsen; John William Sleasman; Beatriz Tavares Costa Carvalho; Antonio Condino-Neto; Eyal Grunebaum; Helen Chapel; Hans Dieter Ochs; Alexandra Hult Filipovich; Mort Cowan; Andrew Gennery; Andrew James Cant; Luigi D Notarangelo; Chaim M RoifmanJournal of Allergy and Clinical Immunology v. 139, n. 4, p. 1282-1292, 2017Philadelphia 2017Localização: ICB - Inst. Ciências Biomédicas (PC ICB BMI SEP 2017 )(Acessar) |
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Material Type: Artigo
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Subcutaneous immunoglobulin. Treatment in chronic inflammatory demyelinating polyradiculo-neuropathyNogués, Martín A ; Varela, Francisco J ; Seminario, Gisela ; Insúa, María C ; Bezrodnik, LilianaMedicina (Buenos Aires), 2016, Vol.76 (1), p.36-39 [Periódico revisado por pares]ArgentinaTexto completo disponível |
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Material Type: Artigo
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COVID-19 Vaccination Responses with Different Vaccine Platforms in Patients with Inborn Errors of ImmunityErra, Lorenzo ; Uriarte, Ignacio ; Colado, Ana ; Paolini, María Virginia ; Seminario, Gisela ; Fernández, Julieta Belén ; Tau, Lorena ; Bernatowiez, Juliana ; Moreira, Ileana ; Vishnopolska, Sebastián ; Rumbo, Martín ; Cassarino, Chiara ; Vijoditz, Gustavo ; López, Ana Laura ; Curciarello, Renata ; Rodríguez, Diego ; Rizzo, Gastón ; Ferreyra, Malena ; Ferreyra Mufarregue, Leila Romina ; Badano, María Noel ; Pérez Millán, María Inés ; Quiroga, María Florencia ; Baré, Patricia ; Ibañez, Itatí ; Pozner, Roberto ; Borge, Mercedes ; Docena, Guillermo ; Bezrodnik, Liliana ; Almejun, María BelénJournal of clinical immunology, 2023-02, Vol.43 (2), p.271-285 [Periódico revisado por pares]New York: Springer USTexto completo disponível |
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8 |
Material Type: Artigo
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Human OTULIN haploinsufficiency impairs cell-intrinsic immunity to staphylococcal α-toxinSpaan, Andras N ; Neehus, Anna-Lena ; Laplantine, Emmanuel ; Staels, Frederik ; Ogishi, Masato ; Seeleuthner, Yoann ; Rapaport, Franck ; Lacey, Keenan A ; Van Nieuwenhove, Erika ; Chrabieh, Maya ; Hum, David ; Migaud, Melanie ; Izmiryan, Araksya ; Lorenzo, Lazaro ; Kochetkov, Tatiana ; Heesterbeek, Dani AC ; Bardoel, Bart W ; DuMont, Ashley L ; Dobbs, Kerry ; Chardonnet, Solenne ; Heissel, Soren ; Baslan, Timour ; Zhang, Peng ; Yang, Rui ; Bogunovic, Dusan ; Wunderink, Herman F ; Haas, Pieter-Jan A ; Molina, Henrik ; Van Buggenhout, Griet ; Lyonnet, Stanislas ; Notarangelo, Luigi D ; Seppanen, Mikko RJ ; Weil, Robert ; Seminario, Gisela ; Gomez-Tello, Hector ; Wouters, Carine ; Mesdaghi, Mehrnaz ; Shahrooei, Mohammad ; Bossuyt, Xavier ; Sag, Erdal ; Topaloglu, Rezan ; Ozen, Seza ; Leavis, Helen L ; van Eijk, Maarten MJ ; Bezrodnik, Liliana ; Galicia, Lizbeth Blancas ; Hovnanian, Alain ; Nassif, Aude ; Bader-Meunier, Brigitte ; Neven, Benedicte ; Meyts, Isabelle ; Schrijvers, Rik ; Puel, Anne ; Bustamante, Jacinta ; Aksentijevich, Ivona ; Kastner, Daniel L ; Torres, Victor J ; Humblet-Baron, Stephanie ; Liston, Adrian ; Abel, Laurent ; Boisson, Bertrand ; Casanova, Jean-LaurentSCIENCE, 2022-06, Vol.376 (6599), p.1285-+ [Periódico revisado por pares]AMER ASSOC ADVANCEMENT SCIENCETexto completo disponível |
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Material Type: Artigo
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Patients with Primary Immunodeficiencies Are a Reservoir of Poliovirus and a Risk to Polio EradicationAghamohammadi, Asghar ; Abolhassani, Hassan ; Kutukculer, Necil ; Wassilak, Steve G ; Pallansch, Mark A ; Kluglein, Samantha ; Quinn, Jessica ; Sutter, Roland W ; Wang, Xiaochuan ; Sanal, Ozden ; Latysheva, Tatiana ; Ikinciogullari, Aydan ; Bernatowska, Ewa ; Tuzankina, Irina A ; Costa-Carvalho, Beatriz T ; Franco, Jose Luis ; Somech, Raz ; Karakoc-Aydiner, Elif ; Singh, Surjit ; Bezrodnik, Liliana ; Espinosa-Rosales, Francisco J ; Shcherbina, Anna ; Lau, Yu-Lung ; Nonoyama, Shigeaki ; Modell, Fred ; Modell, Vicki ; Barbouche, Mohamed-Ridha ; McKinlay, Mark AFrontiers in immunology, 2017-06, Vol.8, p.685-685 [Periódico revisado por pares]Switzerland: FrontiersTexto completo disponível |
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Material Type: Artigo
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Comparative Study of Subcutaneous Versus Intravenous IgG Replacement Therapy in Pediatric Patients with Primary Immunodeficiency Diseases: A Multicenter Study in ArgentinaBezrodnik, Liliana ; Gómez Raccio, Andrea ; Belardinelli, Gabriela ; Regairaz, Lorena ; Díaz Ballve, Damacia ; Seminario, Gisela ; Moreira, Ileana ; Riganti, Carlos ; Cantisano, Claudio ; Díaz, Héctor ; Di Giovanni, DanielaJournal of clinical immunology, 2013-10, Vol.33 (7), p.1216-1222 [Periódico revisado por pares]Boston: Springer USTexto completo disponível |