Result Number | Material Type | Add to My Shelf Action | Record Details and Options |
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1 |
Material Type: Livro
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CartazesPierre Mendell Bebel Abreu; Lo Bianco, JuanBuenos Aires Juan Lo Bianco 2009Localização: FAU - Fac. Arquitetura e Urbanismo (741.6 M521c )(Acessar) |
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2 |
Material Type: Livro
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Pierre MendellPierre Mendell Florian Hufnagl; Ginza Guraffiku Gyararåi.Tokyo Ginza Graphic Gallery 2004Localização: FAU - Fac. Arquitetura e Urbanismo (741.6 W893 v.66 e.2 )(Acessar) |
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3 |
Material Type: Livro
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Le roman policierPierre Boileau 1906-1989 Thomas Narcejac 1908-1998; Gérard Mendel 1930-2004Paris Payot 1964Localização: IEB - Inst. Estudos Brasileiros ACERVO MARLYSE MEYER (MM 801.953 B679r )(Acessar) |
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4 |
Material Type: Artigo
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Miyoshi myopathy and limb girdle muscular dystrophy R2 are the same diseaseMoore, Ursula ; Gordish, Heather ; Diaz-Manera, Jordi ; James, Meredith K. ; Mayhew, Anna G. ; Guglieri, Michela ; Fernandez-Torron, Roberto ; Rufibach, Laura E. ; Feng, Jia ; Blamire, Andrew M. ; Carlier, Pierre G. ; Spuler, Simone ; Day, John W. ; Jones, Kristi J. ; Bharucha-Goebel, Diana X. ; Salort-Campana, Emmanuelle ; Pestronk, Alan ; Walter, Maggie C. ; Paradas, Carmen ; Stojkovic, Tanya ; Mori-Yoshimura, Madoka ; Bravver, Elena ; Pegoraro, Elena ; Lowes, Linda Pax ; Mendell, Jerry R. ; Bushby, Kate ; Straub, VolkerNeuromuscular disorders : NMD, 2021-04, Vol.31 (4), p.265-280 [Periódico revisado por pares]England: Elsevier B.VTexto completo disponível |
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5 |
Material Type: Artigo
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Cardiac and pulmonary findings in dysferlinopathy: A 3‐year, longitudinal studyMoore, Ursula ; Fernandez‐Torron, Roberto ; Jacobs, Marni ; Gordish‐Dressman, Heather ; Diaz‐Manera, Jordi ; James, Meredith K. ; Mayhew, Anna G. ; Harris, Elizabeth ; Guglieri, Michela ; Rufibach, Laura E. ; Feng, Jia ; Blamire, Andrew M. ; Carlier, Pierre G. ; Spuler, Simone ; Day, John W. ; Jones, Kristi J. ; Bharucha‐Goebel, Diana X. ; Salort‐Campana, Emmanuelle ; Pestronk, Alan ; Walter, Maggie C. ; Paradas, Carmen ; Stojkovic, Tanya ; Mori‐Yoshimura, Madoka ; Bravver, Elena ; Pegoraro, Elena ; Lowes, Linda Pax ; Mendell, Jerry R. ; Bushby, Kate ; Bourke, John ; Straub, VolkerMuscle & nerve, 2022-05, Vol.65 (5), p.531-540 [Periódico revisado por pares]Hoboken, USA: John Wiley & Sons, IncTexto completo disponível |
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6 |
Material Type: Artigo
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Expanding the muscle imaging spectrum in dysferlinopathy: description of an outlier population from the classical MRI patternLlansó, Laura ; Moore, Ursula ; Bolano-Diaz, Carla ; James, Meredith ; Blamire, Andrew M. ; Carlier, Pierre G. ; Rufibach, Laura ; Gordish-Dressman, Heather ; Boyle, Georgina ; Hilsden, Heather ; Day, John W. ; Jones, Kristi J. ; Bharucha-Goebel, Diana X. ; Salort-Campana, Emmanuelle ; Pestronk, Alan ; Walter, Maggie C. ; Paradas, Carmen ; Stojkovic, Tanya ; Mori-Yoshimura, Madoka ; Bravver, Elena ; Pegoraro, Elena ; Mendell, Jerry R. ; Straub, Volker ; Díaz-Manera, JordiNeuromuscular disorders : NMD, 2023-04, Vol.33 (4), p.349-357 [Periódico revisado por pares]England: Elsevier B.VTexto completo disponível |
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7 |
Material Type: Artigo
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Myostatin and follistatin as monitoring and prognostic biomarkers in dysferlinopathyMoore, Ursula ; Fernández-Simón, Esther ; Schiava, Marianela ; Cox, Dan ; Gordish-Dressman, Heather ; James, Meredith K. ; Mayhew, Anna ; Wilson, Ian ; Guglieri, Michela ; Rufibach, Laura ; Blamire, Andrew ; Carlier, Pierre G. ; Mori-Yoshimura, Madoka ; Day, John W. ; Jones, Kristi J. ; Bharucha-Goebel, Diana X. ; Salort-Campana, Emmanuelle ; Pestronk, Alan ; Walter, Maggie C. ; Paradas, Carmen ; Stojkovic, Tanya ; Bravver, Elena ; Pegoraro, Elena ; Mendell, Jerry R. ; Bushby, Kate ; Diaz-Manera, Jordi ; Straub, VolkerNeuromuscular disorders : NMD, 2023-02, Vol.33 (2), p.199-207 [Periódico revisado por pares]England: Elsevier B.VTexto completo disponível |
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8 |
Material Type: Artigo
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KIT signaling regulates MITF expression through miRNAs in normal and malignant mast cell proliferationLee, Youl-Nam ; Brandal, Stephanie ; Noel, Pierre ; Wentzel, Erik ; Mendell, Joshua T. ; McDevitt, Michael A. ; Kapur, Reuben ; Carter, Melody ; Metcalfe, Dean D. ; Takemoto, Clifford M.Blood, 2011-03, Vol.117 (13), p.3629-3640 [Periódico revisado por pares]Washington, DC: Elsevier IncTexto completo disponível |
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9 |
Material Type: Artigo
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Teenage exercise is associated with earlier symptom onset in dysferlinopathy: a retrospective cohort studyMoore, Ursula R ; Jacobs, Marni ; Fernandez-Torron, Roberto ; Jang, Jiji ; James, Meredith K ; Mayhew, Anna ; Rufibach, Laura ; Mittal, Plavi ; Eagle, Michelle ; Cnaan, Avital ; Carlier, Pierre G ; Blamire, Andrew ; Hilsden, Heather ; Lochmüller, Hanns ; Grieben, Ulrike ; Spuler, Simone ; Tesi Rocha, Carolina ; Day, John W ; Jones, Kristi J ; Bharucha-Goebel, Diana X ; Salort-Campana, Emmanuelle ; Harms, Matthew ; Pestronk, Alan ; Krause, Sabine ; Schreiber-Katz, Olivia ; Walter, Maggie C ; Paradas, Carmen ; Hogrel, Jean-Yves ; Stojkovic, Tanya ; Takeda, Shin’ichi ; Mori-Yoshimura, Madoka ; Bravver, Elena ; Sparks, Susan ; Diaz-Manera, Jordi ; Bello, Luca ; Semplicini, Claudio ; Pegoraro, Elena ; Mendell, Jerry R ; Bushby, Kate ; Straub, VolkerJournal of neurology, neurosurgery and psychiatry, 2018-11, Vol.89 (11), p.1224-1226 [Periódico revisado por pares]England: BMJ Publishing Group LTDTexto completo disponível |
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10 |
Material Type: Artigo
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Intensive Teenage Activity Is Associated With Greater Muscle Hyperintensity on T1W Magnetic Resonance Imaging in Adults With DysferlinopathyMoore, Ursula ; Jacobs, Marni ; Fernandez-Torron, Roberto ; LLauger Rossello, Jaume ; Smith, Fiona E ; James, Meredith ; Mayhew, Anna ; Rufibach, Laura ; Carlier, Pierre G ; Blamire, Andrew M ; Day, John W ; Jones, Kristi J ; Bharucha-Goebel, Diana X ; Salort-Campana, Emmanuelle ; Pestronk, Alan ; Walter, Maggie C ; Paradas, Carmen ; Stojkovic, Tanya ; Mori-Yoshimura, Madoka ; Bravver, Elena ; Pegoraro, Elena ; Mendell, Jerry R ; Bushby, Kate ; Straub, Volker ; Diaz-Manera, JordiFrontiers in neurology, 2020-12, Vol.11, p.613446-613446 [Periódico revisado por pares]Switzerland: Frontiers Media S.ATexto completo disponível |