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1
Acquired and genetic complement abnormalities play a critical role in dense deposit disease and other C3 glomerulopathies
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Acquired and genetic complement abnormalities play a critical role in dense deposit disease and other C3 glomerulopathies

Servais, Aude ; Noël, Laure-Hélène ; Roumenina, Lubka T. ; Le Quintrec, Moglie ; Ngo, Stephanie ; Dragon-Durey, Marie-Agnès ; Macher, Marie-Alice ; Zuber, Julien ; Karras, Alexandre ; Provot, François ; Moulin, Bruno ; Grünfeld, Jean-Pierre ; Niaudet, Patrick ; Lesavre, Philippe ; Frémeaux-Bacchi, Véronique

Kidney international, 2012-08, Vol.82 (4), p.454-464 [Periódico revisado por pares]

Basingstoke: Elsevier Inc

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2
C3 Glomerulopathy: Clinicopathologic Features and Predictors of Outcome
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C3 Glomerulopathy: Clinicopathologic Features and Predictors of Outcome

Medjeral-Thomas, Nicholas R ; O'Shaughnessy, Michelle M ; O'Regan, John A ; Traynor, Carol ; Flanagan, Michael ; Wong, Limy ; Teoh, Chia Wei ; Awan, Atif ; Waldron, Mary ; Cairns, Tom ; O'Kelly, Patrick ; Dorman, Anthony M ; Pickering, Matthew C ; Conlon, Peter J ; Cook, H Terence

Clinical journal of the American Society of Nephrology, 2014-01, Vol.9 (1), p.46-53 [Periódico revisado por pares]

United States: American Society of Nephrology

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3
C3 glomerulonephritis: clinicopathological findings, complement abnormalities, glomerular proteomic profile, treatment, and follow-up
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C3 glomerulonephritis: clinicopathological findings, complement abnormalities, glomerular proteomic profile, treatment, and follow-up

Sethi, Sanjeev ; Fervenza, Fernando C. ; Zhang, Yuzhou ; Zand, Ladan ; Vrana, Julie A. ; Nasr, Samih H. ; Theis, Jason D. ; Dogan, Ahmet ; Smith, Richard J.H.

Kidney international, 2012-08, Vol.82 (4), p.465-473 [Periódico revisado por pares]

Basingstoke: Elsevier Inc

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4
C5 nephritic factors drive the biological phenotype of C3 glomerulopathies
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C5 nephritic factors drive the biological phenotype of C3 glomerulopathies

Marinozzi, Maria-Chiara ; Chauvet, Sophie ; Le Quintrec, Moglie ; Mignotet, Morgane ; Petitprez, Florent ; Legendre, Christophe ; Cailliez, Mathilde ; Deschenes, Georges ; Fischbach, Michel ; Karras, Alexandre ; Nobili, Francois ; Pietrement, Christine ; Dragon-Durey, Marie-Agnes ; Fakhouri, Fadi ; Roumenina, Lubka T. ; Fremeaux-Bacchi, Veronique

Kidney international, 2017-11, Vol.92 (5), p.1232-1241 [Periódico revisado por pares]

United States: Elsevier Inc

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5
Patterns of Clinical Response to Eculizumab in Patients With C3 Glomerulopathy
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Patterns of Clinical Response to Eculizumab in Patients With C3 Glomerulopathy

Le Quintrec, Moglie ; Lapeyraque, Anne-Laure ; Lionet, Arnaud ; Sellier-Leclerc, Anne-Laure ; Delmas, Yahsou ; Baudouin, Véronique ; Daugas, Eric ; Decramer, Stéphane ; Tricot, Leila ; Cailliez, Mathilde ; Dubot, Philippe ; Servais, Aude ; Mourey-Epron, Catherine ; Pourcine, Franck ; Loirat, Chantal ; Frémeaux-Bacchi, Véronique ; Fakhouri, Fadi

American journal of kidney diseases, 2018-07, Vol.72 (1), p.84-92 [Periódico revisado por pares]

United States: Elsevier Inc

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6
C3 glomerulonephritis and dense deposit disease share a similar disease course in a large United States cohort of patients with C3 glomerulopathy
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Artigo
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C3 glomerulonephritis and dense deposit disease share a similar disease course in a large United States cohort of patients with C3 glomerulopathy

Bomback, Andrew S. ; Santoriello, Dominick ; Avasare, Rupali S. ; Regunathan-Shenk, Renu ; Canetta, Pietro A. ; Ahn, Wooin ; Radhakrishnan, Jai ; Marasa, Maddalena ; Rosenstiel, Paul E. ; Herlitz, Leal C. ; Markowitz, Glen S. ; D’Agati, Vivette D. ; Appel, Gerald B.

Kidney international, 2018-04, Vol.93 (4), p.977-985 [Periódico revisado por pares]

United States: Elsevier Inc

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7
Complement gene variants determine the risk of immunoglobulin-associated MPGN and C3 glomerulopathy and predict long-term renal outcome
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Artigo
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Complement gene variants determine the risk of immunoglobulin-associated MPGN and C3 glomerulopathy and predict long-term renal outcome

Iatropoulos, Paraskevas ; Noris, Marina ; Mele, Caterina ; Piras, Rossella ; Valoti, Elisabetta ; Bresin, Elena ; Curreri, Manuela ; Mondo, Elena ; Zito, Anna ; Gamba, Sara ; Bettoni, Serena ; Murer, Luisa ; Fremeaux-Bacchi, Veronique ; Vivarelli, Marina ; Emma, Francesco ; Daina, Erica ; Remuzzi, Giuseppe

Molecular immunology, 2016-03, Vol.71, p.131-142 [Periódico revisado por pares]

England: Elsevier Ltd

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8
Spectrum of steroid-resistant and congenital nephrotic syndrome in children: the PodoNet registry cohort
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Artigo
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Spectrum of steroid-resistant and congenital nephrotic syndrome in children: the PodoNet registry cohort

Trautmann, Agnes ; Bodria, Monica ; Ozaltin, Fatih ; Gheisari, Alaleh ; Melk, Anette ; Azocar, Marta ; Anarat, Ali ; Caliskan, Salim ; Emma, Francesco ; Gellermann, Jutta ; Oh, Jun ; Baskin, Esra ; Ksiazek, Joanna ; Remuzzi, Giuseppe ; Erdogan, Ozlem ; Akman, Sema ; Dusek, Jiri ; Davitaia, Tinatin ; Özkaya, Ozan ; Papachristou, Fotios ; Firszt-Adamczyk, Agnieszka ; Urasinski, Tomasz ; Testa, Sara ; Krmar, Rafael T ; Hyla-Klekot, Lidia ; Pasini, Andrea ; Özcakar, Z Birsin ; Sallay, Peter ; Cakar, Nilgun ; Galanti, Monica ; Terzic, Joelle ; Aoun, Bilal ; Caldas Afonso, Alberto ; Szymanik-Grzelak, Hanna ; Lipska, Beata S ; Schnaidt, Sven ; Schaefer, Franz

Clinical journal of the American Society of Nephrology, 2015-04, Vol.10 (4), p.592-600 [Periódico revisado por pares]

United States: American Society of Nephrology

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9
Validation of a Histologic Scoring Index for C3 Glomerulopathy
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Validation of a Histologic Scoring Index for C3 Glomerulopathy

Caravaca-Fontán, Fernando ; Trujillo, Hernando ; Alonso, Marina ; Díaz-Encarnación, Montserrat ; Cabello, Virginia ; Ariceta, Gema ; Quintana, Luis F. ; Marco, Helena ; Barros, Xoana ; Ramos, Natalia ; Rodríguez-Mendiola, Nuria ; Cruz, Sonia ; Fernández-Juárez, Gema ; Rodríguez, Eva ; de la Cerda, Francisco ; Pérez de José, Ana ; López, Inmaculada ; Fernández, Loreto ; Pérez Gómez, Vanessa ; Ávila, Ana ; Bravo, Luis ; Lumbreras, Javier ; Allende, Natalia ; Sanchez de la Nieta, Maria Dolores ; Olea, Teresa ; Melgosa, Marta ; Huerta, Ana ; Miquel, Rosa ; Mon, Carmen ; Fraga, Gloria ; de Lorenzo, Alberto ; Draibe, Juliana ; González, Fayna ; Shabaka, Amir ; Illescas, Maria Luisa ; Calvo, Consuelo ; Oviedo, Victoria ; Da Silva, Iara ; Goicoechea de Jorge, Elena ; Caravaca, Francisco ; Praga, Manuel ; Cavero, Teresa ; Sevillano, Ángel ; Gutiérrez, Eduardo ; Morales, Enrique ; González, Lucia ; Camacho Galán, Rafael ; Gabaldón Domínguez, Alejandra ; Garrido, Marta ; Navarro, Alexandra ; Cortés, José Antonio ; Pascual Martin, Alejando ; Pérez-Ebri, M. Luisa ; Cabrera-Pérez, Rocío ; Panizo Santos, Ángel ; Yébenes Gregorio, Laura ; García Fernández, Maria Eugenia ; Gimeno, Javier ; Cannata Ortiz, Pablo ; Roselló Sastre, Esther ; Saiz, Ana ; Salido Ruiz, Eduardo ; Rodríguez, Rosa ; Corbacho Cuevas, Cesáreo ; Crespo, Francisco Díaz ; Arce, Yolanda ; Garcia-Cuerva Calvar, Maria Soledad ; Saus, Carles ; Guerrero Márquez, Carmen ; García-Herrera, Adriana ; Gomà Gallego, Montserrat ; López Álvarez, Dolores ; Meléndez Muñoz, Cristina ; Centeno, Macarena ; Ferri Ñíguez, Belén ; Mosquera Reboredo, Juan ; Vázquez Martul, Eduardo ; Pérez Gutiérrez, Sofía

American journal of kidney diseases, 2021-05, Vol.77 (5), p.684-695.e1 [Periódico revisado por pares]

United States: Elsevier Inc

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10
Clinical Findings, Pathology, and Outcomes of C3GN after Kidney Transplantation
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Clinical Findings, Pathology, and Outcomes of C3GN after Kidney Transplantation

ZAND, Ladan ; LORENZ, Elizabeth C ; COSIO, Fernando G ; FERVENZA, Fernando C ; NASR, Samih H ; GANDHI, Manish J ; SMITHY, Richard J. H ; SETHI, Sanjeev

Journal of the American Society of Nephrology, 2014-05, Vol.25 (5), p.1110-1117 [Periódico revisado por pares]

Washington, DC: American Society of Nephrology

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